Treatment of Vasodilator-resistant Mixed Connective Tissue Disease-associated Pulmonary Arterial Hypertension with Glucocorticoid and Cyclophosphamide

Sugawara, Eri; Kato, Masaru; Hisada, Ryo; Oku, Kenji; Bohgaki, Toshiyuki; Horita, Tetsuya; Yasuda, Shinsuke; Atsumi, Tatsuya

Treatment of Vasodilator-resistant Mixed Connective Tissue Disease-associated Pulmonary Arterial Hypertension with Glucocorticoid and Cyclophosphamide

Sugawara, Eri; Kato, Masaru; Hisada, Ryo et al.

Internal medicine, 2017, 56(4), 445-448

Permalink : https://hdl.handle.net/2115/65665

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アクセス権	open access
URI	https://hdl.handle.net/2115/65665
タイトル	Treatment of Vasodilator-resistant Mixed Connective Tissue Disease-associated Pulmonary Arterial Hypertension with Glucocorticoid and Cyclophosphamide
著者	Sugawara, Eri ; Kato, Masaru ; Hisada, Ryo ; Oku, Kenji ; Bohgaki, Toshiyuki ; Horita, Tetsuya ; Yasuda, Shinsuke ; Atsumi, Tatsuya
著者名 Sugawara, Eri
e-Rad_Researcher 10755896 著者名 Kato, Masaru
著者名 Hisada, Ryo
著者名 Oku, Kenji
著者名 Bohgaki, Toshiyuki
e-Rad_Researcher 50399929 著者名 Horita, Tetsuya
e-Rad_Researcher 00374231 著者名 Yasuda, Shinsuke
e-Rad_Researcher 20301905 著者名 Atsumi, Tatsuya
言語	英語
キーワード	pulmonary arterial hypertension
	mixed connective tissue disease
	glucocorticoid
	intravenous cyclophosphamide
発行日	2017
出版者	The Japanese Society of Internal Medicine
収録物名	Internal medicine
巻(号)	56(4)
ページ	445-448
抄録	Pulmonary arterial hypertension (PAH) associated with systemic lupus erythematosus (SLE) or mixed connective tissue disease (MTCD), in contrast to other types of PAH, may respond to immunosuppressive therapy. Most PAH cases with an immunosuppressant response were in the early stages of the disease (WHO functional class III or less). The present case was a 34-year-old woman with MCTD-associated PAH (WHO functional class IV) who was resistant to a combination of three vasodilators. Afterwards, she was treated with glucocorticoid and cyclophosphamide. This case suggested the potential benefit of immunosuppressants in patients with severe MCTD-associated PAH.
資源タイプ	学術雑誌論文
出版タイプ	Version of Record
権利情報	Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International
PISSN	0918-2918
関連情報 (isIdenticalTo)	出版社版DOI https://doi.org/10.2169/internalmedicine.56.7668